「Enhanced osteoclastogenesis in patients with MSMD due to impaired response to IFN-γ」の関連論文
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Enhanced osteoclastogenesis in patients with MSMD due to impaired response to IFN-γ
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Inherited CARD9 Deficiency in a Child with Invasive Disease Due to Exophiala dermatitidis and Two Older but Asymptomatic Siblings
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Inherited CARD9 Deficiency in a Child with Invasive Disease Due to Exophiala dermatitidis and Two Older but Asymptomatic Siblings
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Clinical and serological features of dermatomyositis and systemic lupus erythematosus patients with autoantibodies to ADAR1
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Genetic and chemical inhibition of IRF5 suppresses pre-existing mouse lupus-like disease
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A novel NCSTN missense mutation in the signal peptide domain causes hidradenitis suppurativa, which has features characteristic of an autoinflammatory keratinization disease
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Paraneoplastic Pemphigus Mimicking Toxic Epidermal Necrolysis Associated with Follicular Lymphoma: Possible Pathological Role of CD8 T Cells.
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Morphea in a Crohn's disease patient undergoing ustekinumab treatment
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Compromised anti-tumor–immune features of myeloid cell components in chronic myeloid leukemia patients
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A systemic form chronic active Epstein-Barr virus infection diagnosed from erythema nodosum-like skin lesions
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Unique reticular hyperkeratotic eruptions seen in a patient with Darier's disease and attention deficit hyperactivity disorder
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Koebner phenomenon seen in a case of drug-induced granular C3 dermatosis
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Increase of tissue factor expression on the surface of peripheral monocytes of patients with chronic spontaneous urticaria
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Increase of tissue factor expression on the surface of peripheral monocytes of patients with chronic spontaneous urticaria
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Severe neurodevelopmental disorder caused by an MEF2C nonsense mutation
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Squamous Cell Carcinoma at the Site of Cutaneous Lymphoid Hyperplasia
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Increased expression of programmed cell death ligand 1 and galectin 9 in transplant recipients who achieved tolerance after immunosuppression withdrawal
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Hereditary Mucoepithelial Dysplasia and Autosomal-Dominant IFAP Syndrome Is a Clinical Spectrum Due to SREBF1 Variants
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Incontinentia pigmenti in a female infant with somatic mosaicism due to the IKBKG variant
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Detailed analysis of Japanese patients with adenosine deaminase 2 deficiency reveals characteristic elevation of type II interferon signature and STAT1 hyperactivation
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Subacute cutaneous lupus erythematosus with melanocyte elimination induced by pembrolizumab
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Autoantibodies against the plakin family proteins as a novel marker for chronic graft-versus-host disease of the lung
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Identification of a novel causative mutation in KRT1 in diffuse palmoplantar keratoderma, facilitated by whole-exome sequencing
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Successful dupilumab treatment for ichthyotic and atopic features of Netherton syndrome
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A case of systemic lupus erythematosus/systemic sclerosis overlap syndrome successfully treated with belimumab
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Increased blood group 2 innate lymphoid cells are associated with the clinical severity of Kimura disease.
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Clinical Significance of Serum Galectin-9 and Soluble CD155 Levels in Patients with Systemic Sclerosis
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In situ vaccination using unique TLR9 ligand K3-SPG induces long-lasting systemic immune response and synergizes with systemic and local immunotherapy
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Extensive multiple organ involvement in VEXAS syndrome
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Suppression of Systemic Lupus Erythematosus in NZBWF1 mice infected with Hymenolepis microstoma
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Spontaneous regression of hidroacanthoma simplex after skin biopsy
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Osteoprotegerin Prevents Intracranial Aneurysm Progression by Promoting Collagen Biosynthesis and Vascular Smooth Muscle Cell Proliferation
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The fruits of CD40 research in basic and clinical medicine will soon be harvested
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Recurrent palmoplantar pustulosis at the site of insertion of therapeutic titanium
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Association of Local Intrapulmonary Production of Antibodies Specific to Donor Major Histocompatibility Complex Class I With the Progression of Chronic Rejection of Lung Allografts
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Occurrence of cholangiocarcinoma, three years after negative seroconversion of anti-TIF1γ antibody, in a dermatomyositis patient
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Pluripotent stem cell model of Shwachman-Diamond syndrome reveals apoptotic predisposition of hemoangiogenic progenitors
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Interferon-γ enhances the therapeutic effect of mesenchymal stem cells on experimental renal fibrosis
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Interferon-γ enhances the therapeutic effect of mesenchymal stem cells on experimental renal fibrosis
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Irradiation Accelerates Plaque Formation and Cellular Senescence in Flow-Altered Carotid Arteries of Apolipoprotein E Knock-Out Mice
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CD4/CD8 double-negative T-cell lymphoma successfully treated with a combination of bexarotene and total skin electron beam therapy
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Homozygous variant p.Ser427Pro in PNPLA1 is a preventive factor from atopic dermatitis
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Tenascin C Aggravates Autoimmune Myocarditis via Dendritic Cell Activation and Th17 Cell Differentiation
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A case of skin rash during oral administration of a novel androgen receptor inhibitor, darolutamide
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Identification of an Anti-Integrin αvβ6 Autoantibody in Patients With Ulcerative Colitis
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A Novel CD135⁺ Subset of Mouse Monocytes with a Distinct Differentiation Pathway and Antigen-Presenting Properties
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The lectin-like domain of thrombomodulin is a drug candidate for both prophylaxis and treatment of liver ischemia and reperfusion injury in mice
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Constitutively active signaling of MDA5 in Treg cells causes apoptosis of Treg cells and results in autoimmune diseases
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Single-cell transcriptomics of human cholesteatoma identifies an activin A-producing osteoclastogenic fibroblast subset inducing bone destruction
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Comprehensive genomics in androgen receptor-dependent castration-resistant prostate cancer identifies an adaptation pathway mediated by opioid receptor kappa 1