「iPS cells from Chediak-Higashi syndrome patients recapitulate the giant granules in myeloid cells」の関連論文
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Pluripotent stem cell model of Shwachman-Diamond syndrome reveals apoptotic predisposition of hemoangiogenic progenitors
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N-Acetylcysteine prevents amyloid-β secretion in neurons derived from human pluripotent stem cells with trisomy 21
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Generation of macrophages with altered viral sensitivity from genome-edited rhesus macaque iPSCs to model human disease
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Malfunctioning CD106-positive, short-term hematopoietic stem cells trigger diabetic neuropathy in mice by cell fusion.
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Quality assessment tests for tumorigenicity of human iPS cell-derived cartilage
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Compromised anti-tumor–immune features of myeloid cell components in chronic myeloid leukemia patients
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A disease-specific iPS cell resource for studying rare and intractable diseases
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Three-dimensional human placenta-like bud synthesized from induced pluripotent stem cells
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Cryptotanshinone is a candidate therapeutic agent for interstitial lung disease associated with a BRICHOS-domain mutation of SFTPC
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Dermal fibroblast-like cells reprogrammed directly from adipocytes in mouse (本文)
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In vivo regeneration of interspecies chimeric kidneys using a nephron progenitor cell replacement system
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Simple derivation of skeletal muscle from human pluripotent stem cells using temperature‐sensitive Sendai virus vector
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Bone marrow-derived inducible microglia-like cells ameliorate motor function and survival in a mouse model of amyotrophic lateral sclerosis.
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Azacitidine is a potential therapeutic drug for pyridoxine-refractory female X-linked sideroblastic anemia
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Prophylactic treatment of rapamycin ameliorates naturally developing and episode -induced heterotopic ossification in mice expressing human mutant ACVR1
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A novel cancer immunotherapy using tumor-infiltrating B cells in the APC (min/+) mouse model
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Production and nonclinical evaluation of an autologous iPSC-derived platelet product for the iPLAT1 clinical trial
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One-step induction of photoreceptor-like cells from human iPSCs by delivering transcription factors
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Identification of CXCL12-abundant reticular cells in human adult bone marrow
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Recapitulation of pro-inflammatory signature of monocytes with ACVR1A mutation using FOP patient-derived iPSCs
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Improved Sendai viral system for reprogramming to naive pluripotency
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Antifibrotic effect of lung-resident progenitor cells with high aldehyde dehydrogenase activity
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Antifibrotic effect of lung-resident progenitor cells with high aldehyde dehydrogenase activity
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Mature Myotubes Generated From Human-Induced Pluripotent Stem Cells Without Forced Gene Expression
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iPSC-derived type IV collagen α5-expressing kidney organoids model Alport syndrome
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Smooth muscle protein 22α‐Cre recombination in resting cardiac fibroblasts and hematopoietic precursors
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Gene Editing in Murine Hematopoietic Stem Cells Using a Novel Ex Vivo Expansion System
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Differentiation of Human Induced Pluripotent Stem Cells Into Testosterone-Producing Leydig-like Cells
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Generation of two human induced pluripotent stem cell lines derived from two X-linked adrenoleukodystrophy patients with ABCD1 mutations
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Constitutive activation of mTORC1 signaling induced by biallelic loss-of-function mutations in SZT2 underlies a discernible neurodevelopmental disease
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GLT1 gene delivery based on bone marrow-derived cells ameliorates motor function and survival in a mouse model of ALS.
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Collagen X Is Dispensable for Hypertrophic Differentiation and Endochondral Ossification of Human iPSC-Derived Chondrocytes
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Characterization and reduction of non-endocrine cells accompanying islet-like endocrine cells differentiated from human iPSC
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Characterization of hiPSC-Derived Muscle Progenitors Reveals Distinctive Markers for Myogenic Cell Purification Toward Cell Therapy
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iPSC-derived mesenchymal cells that support alveolar organoid development
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Tenascin C Aggravates Autoimmune Myocarditis via Dendritic Cell Activation and Th17 Cell Differentiation
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Enhancing the Therapeutic Efficacy of Bone Marrow-Derived Mononuclear Cells with Growth Factor-Expressing Mesenchymal Stem Cells for ALS in Mice.
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Cryopreservation of Induced Pluripotent Stem Cell-Derived Dopaminergic Neurospheres for Clinical Application
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Single-cell transcriptomics of human cholesteatoma identifies an activin A-producing osteoclastogenic fibroblast subset inducing bone destruction
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Lineage tracing analysis defines erythropoietin-producing cells as a distinct subpopulation of resident fibroblasts with unique behaviors
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Development of platelet replacement therapy using human induced pluripotent stem cells
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高純度間葉系幹細胞は機能的ミトコンドリア投入に優れている
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Multi-omics approach reveals post-transcriptionally regulated genes are essential for human pluripotent stem cells
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Embryonal erythropoiesis and aging exploit ferroptosis
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Engraftment of allogeneic iPS cell-derived cartilage organoid in a primate model of articular cartilage defect
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Enhanced chondrogenic differentiation of iPS cell-derived mesenchymal stem/stromal cells via neural crest cell induction for hyaline cartilage repair
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Ebf3⁺ niche-derived CXCL12 is required for the localization and maintenance of hematopoietic stem cells
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Genomic stability of mouse spermatogonial stem cells in vitro
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DMRT1-mediated reprogramming drives development of cancer resembling human germ cell tumors with features of totipotency
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Studies on the pathological mechanism of alopecia areata in C3H/HeJ mouse model