「ERRγ agonist under mechanical stretching manifests hypertrophic cardiomyopathy phenotypes of engineered cardiac tissue through maturation」の関連論文
-
ERRγ enhances cardiac maturation with T-tubule formation in human iPSC-derived cardiomyocytes
-
SMN promotes mitochondrial metabolic maturation during myogenesis by regulating the MYOD-miRNA axis
-
Immunosuppressants Tacrolimus and Sirolimus revert the cardiac antifibrotic properties of p38-MAPK inhibition in 3D-multicellular human iPSC-heart organoids
-
Mature Myotubes Generated From Human-Induced Pluripotent Stem Cells Without Forced Gene Expression
-
Lionheart LincRNA alleviates cardiac systolic dysfunction under pressure overload
-
Disrupted Cav1.2 Selectivity Causes Overlapping Long QT and Brugada Syndrome Phenotypes in CACNA1C-E1115K iPS Cell Model
-
Hydrostatic pressure suppresses fibrotic changes via Akt/GSK‐3 signaling in human cardiac fibroblasts
-
Human induced pluripotent stem cells generated from a patient with idiopathic basal ganglia calcification
-
Differentiation of hypertrophic chondrocytes from human iPSCs for the in vitro modeling of chondrodysplasias
-
Establishment of quantitative and consistent in vitro skeletal muscle pathological models of myotonic dystrophy type 1 using patient-derived iPSCs
-
A muscle fatigue-like contractile decline was recapitulated using skeletal myotubes from Duchenne muscular dystrophy patient-derived iPSCs
-
Pluripotent stem cell model of Shwachman-Diamond syndrome reveals apoptotic predisposition of hemoangiogenic progenitors
-
Cryptotanshinone is a candidate therapeutic agent for interstitial lung disease associated with a BRICHOS-domain mutation of SFTPC
-
Circulatory C-type natriuretic peptide reduces mucopolysaccharidosis-associated craniofacial hypoplasia in vivo
-
Fibrosis growth factor 23 is a promoting factor for cardiac fibrosis in the presence of transforming growth factor-b1
-
N-Acetylcysteine prevents amyloid-β secretion in neurons derived from human pluripotent stem cells with trisomy 21
-
Prophylactic treatment of rapamycin ameliorates naturally developing and episode -induced heterotopic ossification in mice expressing human mutant ACVR1
-
Collagen X Is Dispensable for Hypertrophic Differentiation and Endochondral Ossification of Human iPSC-Derived Chondrocytes
-
Establishment of a heart‐on‐a‐chip microdevice based on human iPS cells for the evaluation of human heart tissue function
-
Tenascin C Aggravates Autoimmune Myocarditis via Dendritic Cell Activation and Th17 Cell Differentiation
-
iPSC-derived type IV collagen α5-expressing kidney organoids model Alport syndrome
-
Malfunctioning CD106-positive, short-term hematopoietic stem cells trigger diabetic neuropathy in mice by cell fusion.
-
Am80, a retinoic acid receptor agonist, activates the cardiomyocyte cell cycle and enhances engraftment in the heart
-
Azacitidine is a potential therapeutic drug for pyridoxine-refractory female X-linked sideroblastic anemia
-
Cell migration is impaired in XPA-deficient cells
-
Dilated cardiomyopathy-linked heat shock protein family D member 1 mutations cause up-regulation of reactive oxygen species and autophagy through mitochondrial dysfunction (本文)
-
One-step induction of photoreceptor-like cells from human iPSCs by delivering transcription factors
-
Myh9 R702C is associated with erythroid abnormality with splenomegaly in mice
-
Effect of prolonged culture and hypoxic conditions on in vitro neural differentiation potency of embryonic stem cell-derived neural stem cells
-
Study of Mitochonic Acid 5 to improve neuromuscular dysfunction associated with aging and diseases using C. elegans
-
TEAD1 trapping by the Q353R–Lamin A/C causes dilated cardiomyopathy
-
Generation of two human induced pluripotent stem cell lines derived from two X-linked adrenoleukodystrophy patients with ABCD1 mutations
-
Novel Therapeutic Impact of Isorhamnetin for the Upstream Treatment of Atrial Fibrillation
-
Studies on Prediction of Cardiotoxicity Induced by Anticancer Drugs and Exploration of Molecular Targets to Prevent Cardiotoxicity
-
Functional rejuvenation of aged neural stem cells by Plagl2 and anti-Dyrk1a activity
-
Cellular senescence in white matter microglia is induced during ageing in mice and exacerbates the neuroinflammatory phenotype
-
Enhanced chondrogenic differentiation of iPS cell-derived mesenchymal stem/stromal cells via neural crest cell induction for hyaline cartilage repair
-
Analysis of disease model iPSCs derived from patients with a novel Fanconi anemia-like IBMFS ADH5/ALDH2 deficiency
-
Orai1–STIM1 Regulates Increased Ca²⁺ Mobilization, Leading to Contractile Duchenne Muscular Dystrophy Phenotypes in Patient-Derived Induced Pluripotent Stem Cells
-
Recapitulation of pro-inflammatory signature of monocytes with ACVR1A mutation using FOP patient-derived iPSCs
-
Expression dynamics of HAND1/2 in in vitro human cardiomyocyte differentiation
-
Myogenetic oligodeoxynucleotide (myoDN) recovers the differentiation of skeletal muscle myoblasts deteriorated by diabetes mellitus.
-
Stimulation of myogenesis by ascorbic acid and capsaicin
-
Simple derivation of skeletal muscle from human pluripotent stem cells using temperature‐sensitive Sendai virus vector
-
Constitutive activation of mTORC1 signaling induced by biallelic loss-of-function mutations in SZT2 underlies a discernible neurodevelopmental disease
-
Complex roles of the actin-binding protein Girdin/GIV in DNA damage-induced apoptosis of cancer cells
-
Extracellular vesicles synchronize cellular phenotypes of differentiating cells
-
Grafting of iPS cell-derived tenocytes promotes motor function recovery after Achilles tendon rupture
-
The generation and insights of an inducible diabetes mellitus mouse model based on MafA and MafB double knockout
-
Senescence-associated secretory phenotype promotes chronic ocular graft-vs-host disease in mice and humans (本文)