「iPSC-derived type IV collagen α5-expressing kidney organoids model Alport syndrome」の関連論文
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Prophylactic treatment of rapamycin ameliorates naturally developing and episode -induced heterotopic ossification in mice expressing human mutant ACVR1
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Differentiation of hypertrophic chondrocytes from human iPSCs for the in vitro modeling of chondrodysplasias
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Circulatory C-type natriuretic peptide reduces mucopolysaccharidosis-associated craniofacial hypoplasia in vivo
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Human iPSC-derived renal collecting duct organoid model cystogenesis in ADPKD
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Cryptotanshinone is a candidate therapeutic agent for interstitial lung disease associated with a BRICHOS-domain mutation of SFTPC
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In vivo regeneration of interspecies chimeric kidneys using a nephron progenitor cell replacement system
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N-Acetylcysteine prevents amyloid-β secretion in neurons derived from human pluripotent stem cells with trisomy 21
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Malfunctioning CD106-positive, short-term hematopoietic stem cells trigger diabetic neuropathy in mice by cell fusion.
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A muscle fatigue-like contractile decline was recapitulated using skeletal myotubes from Duchenne muscular dystrophy patient-derived iPSCs
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Immunosuppressants Tacrolimus and Sirolimus revert the cardiac antifibrotic properties of p38-MAPK inhibition in 3D-multicellular human iPSC-heart organoids
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Mature Myotubes Generated From Human-Induced Pluripotent Stem Cells Without Forced Gene Expression
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Pluripotent stem cell model of Shwachman-Diamond syndrome reveals apoptotic predisposition of hemoangiogenic progenitors
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Bioengineering and Cell-derived Strategies for Salivary Gland Regeneration
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Transplantation of human iPSC-derived muscle stem cells in the diaphragm of Duchenne muscular dystrophy model mice
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Quality assessment tests for tumorigenicity of human iPS cell-derived cartilage
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Collagen X Is Dispensable for Hypertrophic Differentiation and Endochondral Ossification of Human iPSC-Derived Chondrocytes
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Human induced pluripotent stem cells generated from a patient with idiopathic basal ganglia calcification
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StemPanTox: a fast and wide-target drug assessment system for tailor-made safety evaluations using personalized iPS cells
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iPSC technology-based regenerative medicine for kidney diseases
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Establishment of a heart‐on‐a‐chip microdevice based on human iPS cells for the evaluation of human heart tissue function
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One-step induction of photoreceptor-like cells from human iPSCs by delivering transcription factors
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Studies on the pathological mechanism of alopecia areata in C3H/HeJ mouse model
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Gut contractile organoids: a novel model system to study the cellular synchronization in gastrointestinal motility
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Generation of two human induced pluripotent stem cell lines derived from two X-linked adrenoleukodystrophy patients with ABCD1 mutations
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Human bone marrow-derived mesenchymal stromal cells cultured in serum-free media demonstrate enhanced antifibrotic abilities via prolonged survival and robust regulatory T cell induction in murine bleomycin-induced pulmonary fibrosis
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Human bone marrow-derived mesenchymal stromal cells cultured in serum-free media demonstrate enhanced antifibrotic abilities via prolonged survival and robust regulatory T cell induction in murine bleomycin-induced pulmonary fibrosis
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Three-dimensional spheroid culture induces apical-basal polarity and the original characteristics of immortalized human renal proximal tubular epithelial cells
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Pluripotent stem cell-based therapies and their path to the clinic
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Lineage tracing analysis defines erythropoietin-producing cells as a distinct subpopulation of resident fibroblasts with unique behaviors
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Telencephalon Organoids Derived from an Individual with ADHD Show Altered Neurodevelopment of Early Cortical Layer Structure
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Interferon-γ enhances the therapeutic effect of mesenchymal stem cells on experimental renal fibrosis
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Interferon-γ enhances the therapeutic effect of mesenchymal stem cells on experimental renal fibrosis
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Patient-derived ovarian cancer organoids capture the genomic profiles of primary tumours applicable for drug sensitivity and resistance testing (本文)
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A novel cancer immunotherapy using tumor-infiltrating B cells in the APC (min/+) mouse model
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Reverse Genetic Studies on Mitochondrial tRNA-related Disorders
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Single-cell transcriptomics of human cholesteatoma identifies an activin A-producing osteoclastogenic fibroblast subset inducing bone destruction
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Recapitulation of pro-inflammatory signature of monocytes with ACVR1A mutation using FOP patient-derived iPSCs
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Development of platelet replacement therapy using human induced pluripotent stem cells
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Sarcomatoid mesothelioma diagnosed in a patient with mesothelioma in situ: a case report on morphologic differences after 9-month interval with details analysis of cytology in early-stage mesothelioma
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Constitutive activation of mTORC1 signaling induced by biallelic loss-of-function mutations in SZT2 underlies a discernible neurodevelopmental disease
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Reproducible production and image-based quality evaluation of retinal pigment epithelium sheets from human induced pluripotent stem cells
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STAT3 induces hypoxic preconditioning against oxidative stress in neural stem cells
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2-nitroimidazoles induce mitochondrial stress and ferroptosis in glioma stem cells residing in a hypoxic niche (本文)
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Thrombomodulin ameliorates transforming growth factor-β1-mediated chronic kidney disease via the G-protein coupled receptor 15/Akt signal pathway
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Generation of macrophages with altered viral sensitivity from genome-edited rhesus macaque iPSCs to model human disease
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Clinical and Basic Research for Ovarian Cancer
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Antifibrotic effect of lung-resident progenitor cells with high aldehyde dehydrogenase activity
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Antifibrotic effect of lung-resident progenitor cells with high aldehyde dehydrogenase activity
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Azacitidine is a potential therapeutic drug for pyridoxine-refractory female X-linked sideroblastic anemia
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Functional and genomic characterization of patient-derived xenograft model to study adaptation to mTORC1 inhibitor in clear cell renal cell carcinoma