「The stimulator of interferon genes (STING) pathway is upregulated in striatal astrocytes of patients with multiple system atrophy」の関連論文
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Altered functional connectivity associated with striatal dopamine depletion in Parkinson’s disease
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Characteristics of cortical spreading depression and c-Fos expression in transgenic mice having a mutation associated with familial hemiplegic migraine 2 (本文)
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Is Generalized and Segmental Dystonia Accompanied by Impairments in the Dopaminergic System?
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Human induced pluripotent stem cells generated from a patient with idiopathic basal ganglia calcification
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Discrepancy between distribution of alpha-synuclein oligomers and Lewy-related pathology in Parkinson’s disease
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Aberrant interaction between FUS and SFPQ in neurons in a wide range of FTLD spectrum diseases
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Pattern of THK 5351 retention in normal aging involves core regions of resting state networks associated with higher cognitive function
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Pharmacological Studies on the Roles of M1 Muscarinic Acetylcholine Receptors in the Cognitive Function of the Rodent Brain
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SAK3 Administration Improves Spine Abnormalities and Cognitive Deficits in AppNL-G-F/NL-G-F Knock-in Mice by Increasing Proteasome Activity through CaMKII/Rpt6 Signaling
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A clinical and genetic study of SPG31 in Japan
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Paraproteinemia and neuropathy
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LC3/FtMt Colocalization Patterns Reveal the Progression of FtMt Accumulation in Nigral Neurons of Patients with Progressive Supranuclear Palsy.
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Optimized sonoreactor for accelerative amyloid-fibril assays through enhancement of primary nucleation and fragmentation
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Serum neurofilament light chain in chronic inflammatory demyelinating polyneuropathy
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Motor Progression and Nigrostriatal Neurodegeneration in Parkinson Disease
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Molecular genetic study of the FMR1 CGG repeat configurations in the Japanese population and patients with Fragile X-Associated Tremor/Ataxia Syndrome
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Labyrinthine calcification in ears with otitis media and antineutrophil cytoplasmic antibody-associated vasculitis (OMAAV): A report of two cases
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Case report: Late middle-aged features of FAM111A variant, Kenny–Caffey syndrome type 2-suggestive symptoms during a long follow-up
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Interactions of amyloid coaggregates with biomolecules and its relevance to neurodegeneration
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Failure of internal fixation for ankle joint Charcot neuroarthropathy with beta(2)-microglobulin amyloidosis: a case report
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Cell migration is impaired in XPA-deficient cells
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Successful treatment of a novel type I interferonopathy due to a de novo PSMB9 gene mutation with a Janus kinase inhibitor
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Morphological changes of large layer V pyramidal neurons in cortical motor-related areas after spinal cord injury in macaque monkeys
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Neuroinflammation in neurodegenerative disease
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Anti-Epileptic Effects of FABP3 Ligand MF1 through the Benzodiazepine Recognition Site of the GABAA Receptor.
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UBAP1 mutations cause juvenile-onset hereditary spastic paraplegias (SPG80) and impair UBAP1 targeting to endosomes
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A cerebrospinal fluid microRNA analysis: Progressive supranuclear palsy
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α-Synuclein BAC transgenic mice exhibit RBD-like behaviour and hyposmia: a prodromal Parkinson’s disease model
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Case report: Severe non-pigmenting fixed drug eruption showing general symptoms caused by chondroitin sulfate sodium
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Medial prefrontal area reductions, altered expressions of cholecystokinin, parvalbumin, and activating transcription factor 4 in the corticolimbic system, and altered emotional behavior in a progressive rat model of type 2 diabetes
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Medial prefrontal area reductions, altered expressions of cholecystokinin, parvalbumin, and activating transcription factor 4 in the corticolimbic system, and altered emotional behavior in a progressive rat model of type 2 diabetes
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Elderly patient with 5q spinal muscular atrophy type 4 markedly improved by Nusinersen
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Glucose transporter Glut1 controls diffuse invasion phenotype with perineuronal satellitosis in diffuse glioma microenvironment
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FKRP mutations cause congenital muscular dystrophy 1C and limb-girdle muscular dystrophy 2I in Asian patients
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Physiological and Pathological Mitochondrial Clearance Is Related to Pectoralis Major Muscle Pathogenesis in Broilers With Wooden Breast Syndrome
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Optimal conditions for graft survival and reinnervation of denervated muscles after embryonic motoneuron transplantation into peripheral nerves undergoing Wallerian degeneration
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The relationship between DRD2 Taq1A polymorphism and white matter structure in healthy young adults.
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Exacerbation of epilepsy by astrocyte alkalization and gap junction uncoupling.
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TNFRSF11A-Associated Dysosteosclerosis: A Report of the Second Case and Characterization of the Phenotypic Spectrum
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Iinfluence of plasma cytokine levels on the conversion risk from MCI to dementia in the Alzheimer's disease neuroimaging initiative database
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Pathological gait in Rett syndrome: Quantitative evaluation using three-dimensional gait analysis
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Centronuclear Myopathy with Abundant Nemaline Rods in a Japanese Black and Hereford Crossbred Calf
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Prickle2 and Igsf9b coordinately regulate the cytoarchitecture of the axon initial segment
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Tooth Loss Induces Memory Impairment and Gliosis in App Knock-in Mouse Models of Alzheimer's disease
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Myelodysplastic syndrome with trisomy 8 presenting periodic fever and multiple MEFV gene variants outside exon 10: a case report
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Potential role of administration of menaquinone-4 and its chemically related compound for neuroinflammatory modulation
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Rescue of recurrent deep intronic mutation underlying cell type-dependent quantitative NEMO deficiency
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Circulatory C-type natriuretic peptide reduces mucopolysaccharidosis-associated craniofacial hypoplasia in vivo
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Stress-Related Neuronal Clusters in Sublenticular Extended Amygdala of Basal Forebrain Show Individual Differences of Positions
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Alterations in DNA methylation rates of brain-derived neurotrophic factor in patients with schizophrenia.