「Daple deficiency causes hearing loss in adult mice by inducing defects in cochlear stereocilia and apical microtubules」の関連論文
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Knock-in mice bearing constitutively active αIIb(R990W) mutation develop macrothrombocytopenia with severe platelet dysfunction
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Modeling reduced contractility and impaired desmosome assembly due to plakophilin-2 deficiency using isogenic iPS cell-derived cardiomyocytes
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Nexin-Dynein regulatory complex component DRC7 but not FBXL13 is required for sperm flagellum formation and male fertility in mice
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Phosphorylation of MYL12 by Myosin Light Chain Kinase Regulates Cellular Shape Changes in Cochlear Hair Cells
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Aberrant accumulation of TMEM43 accompanied by perturbed transmural gene expression in arrhythmogenic cardiomyopathy
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Pharmacotherapy alleviates pathological changes in human direct reprogrammed neuronal cell model of myotonic dystrophy type 1
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Single-nucleus RNA sequencing identified cells with ependymal cell-like features enriched in neonatal mice after spinal cord injury
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Anti-AQP4 autoantibodies promote ATP release from astrocytes and induce mechanical pain in rats
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Dietary salt with nitric oxide deficiency induces nocturnal polyuria in mice via hyperactivation of intrarenal angiotensinⅡ-SPAK-NCC pathway
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Insulinoma induces a hyperinsulinemia-mediated decrease of GLUT2 and GLP1 receptor in normal pancreatic β-cells
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Implantation of human iPS cell-derived cartilage in bone defects of mice
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The CD153 vaccine is a senotherapeutic option for preventing the accumulation of senescent T cells in mice
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Dysregulated Expression of the Nuclear Exosome Targeting Complex Component Rbm7 in Nonhematopoietic Cells Licenses the Development of Fibrosis
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4-Phenylbutyrate ameliorates apoptotic neural cell death in Down syndrome by reducing protein aggregates
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Hyperglycemia enhances pancreatic cancer progression accompanied by elevations in phosphorylated STAT3 and MYC levels
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Combined effect of teriparatide and an anti-RANKL monoclonal antibody on bone defect regeneration in mice with glucocorticoid-induced osteoporosis
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Evidence that TD-198946 enhances the chondrogenic potential of human synovium-derived stem cells through the NOTCH3 signaling pathway
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Inhibition of Clusterin Represses Proliferation by Inducing Cellular Senescence in Pancreatic Cancer
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Signal-transducing adapter protein-1 is required for maintenance of leukemic stem cells in CML
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CAG repeat-binding small molecule improves motor coordination impairment in a mouse model of Dentatorubral-pallidoluysian atrophy
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Local sympathetic neurons promote neutrophil egress from the bone marrow at the onset of acute inflammation
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Expression of polydom in dermal neurofibroma and surrounding dermis in von Recklinghausen’s disease
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A human isogenic iPSC-derived cell line panel identifies major regulators of aberrant astrocyte proliferation in Down syndrome
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Increased vascular permeability and severe renal tubular damage after ischemia-reperfusion injury in mice lacking adiponectin or T-cadherin
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Adiponectin accumulation in the retinal vascular endothelium and its possible role in preventing early diabetic microvascular damage
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ADAR1 regulates early T cell development via MDA5-dependent and -independent pathways
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The lysosomal Ragulator complex plays an essential role in leukocyte trafficking by activating myosin II
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Suppression of autophagy promotes fibroblast activation in p53-deficient colorectal cancer cells
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Targeted sensory reinnervation by direct neurotization of skin: An experimental study in rats
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SCYL1 arginine methylation by PRMT1 is essential for neurite outgrowth via Golgi morphogenesis
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Intravital Imaging Reveals the Ameliorating Effect of Colchicine in a Photothrombotic Stroke Model via Inhibition of Neutrophil Recruitment
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Notch Signaling-modified Mesenchymal Stem Cells Improve Tissue Perfusion by Induction of Arteriogenesis in a Rat Hindlimb Ischemia Model
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Pemafibrate suppresses NLRP3 inflammasome activation in the liver and heart in a novel mouse model of steatohepatitis-related cardiomyopathy
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Ectonucleotidase CD39 is highly expressed on ATLL cells and is responsible for their immunosuppressive function
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APR-246 induces apoptosis and enhances chemo-sensitivity via activation of ROS and TAp73-Noxa signal in oesophageal squamous cell cancer with TP53 missense mutation
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Postsynaptic structure formation of human iPS cell-derived neurons takes longer than presynaptic formation during neural differentiation in vitro
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Glucotoxicity-induced suppression of Cox6a2 expression provokes β-cell dysfunction via augmented ROS production
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Go-sha-jinki-Gan Alleviates Inflammation in Neurological Disorders via p38-TNF Signaling in the Central Nervous System
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Phenotypic recapitulation and correction of desmoglein-2-deficient cardiomyopathy using human-induced pluripotent stem cell-derived cardiomyocytes
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Scaffold-Mediated Developmental Effects on Human Induced Pluripotent Stem Cell-Derived Cardiomyocytes Are Preserved After External Support Removal
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Engineered clustered myoblast cell injection augments angiogenesis and muscle regeneration in peripheral artery disease
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Activation of p53 after irradiation impairs the regenerative capacity of the mouse liver
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Efficient Differentiation of Mouse Induced Pluripotent Stem Cells into Alveolar Epithelium Type II with a BRD4 Inhibitor
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Reduction of Cell Surface T-Cell Receptor by Non-Mitogenic CD3 Antibody to Mitigate Murine Lupus
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Age-dependent loss of adipose Rubicon promotes metabolic disorders via excess autophagy
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Ocular fixations and presaccadic potentials to explain pareidolias in Parkinson's disease
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Loss-of-function mutations in the co-chaperone protein BAG5 cause dilated cardiomyopathy requiring heart transplantation
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Tet DNA demethylase is required for plasma cell differentiation by controlling expression levels of IRF4
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RGMa Signal in Macrophages Induces Neutrophil-Related Astrocytopathy in NMO
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Decreased YAP activity reduces proliferative ability in human induced pluripotent stem cell of duchenne muscular dystrophy derived cardiomyocytes